Gastroenterology Research, ISSN 1918-2805 print, 1918-2813 online, Open Access
Article copyright, the authors; Journal compilation copyright, Gastroenterol Res and Elmer Press Inc
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Case Report

Volume 5, Number 2, April 2012, pages 63-66

A Case of Congenital Hepatic Fibrosis Associated With Medullary Sponge Kidney-Radiologic and Pathologic Features

Figures

Figure 1.
Figure 1. A: Abdominal enhanced CT scan, dilated intra-hepatic bile ducts (red arrow) and hepatosplenomegaly; B: Splenomegaly, circuitous spleen vein (short red arrow), and medullary sponge kidney (long red arrow).
Figure 2.
Figure 2. A: CT angiography of visceral vascular, tortuous thickening spleen vein (short white arrow) and proximal portal vein (long white arrow); B: Reconstruction of CT angiography, hepatomegaly (red arrowhead), splenomegaly (long red arrow), circuitous thickening spleen and portal vein (short red arrow).
Figure 3.
Figure 3. A: Pathology of liver biopsy sample, extensively swelling hepatocytes, and few necrosis hepatocytes. No fat denaturalization and no apoptosis (HE x 200); B: Pathology of liver biopsy sample, significant hyperplasia of fibrous connective tissues (black arrow), and hyperplasia of bile ductules (green arrow). No inflammatory cellular infiltration (HE x 200); C: Pathology of liver biopsy sample: formation of integrated fibrosis interval septum (short arrow) (HE x 100); D: Pathology of liver biopsy sample, dilated hyperplasia of bile ductules (red arrow) and flattening epithelium. No sedimentation of amyloid (HE x 200).